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Epidermolysis bullosa acquisita with oesophageal stenosis
Author(s) -
MIYAGAWA SACHIKO,
IIAD TAKASHI,
HACHISUKA HIROSHI,
YAMASHINA YUKIO,
SHIRAI TOSHIHIKO
Publication year - 1992
Publication title -
british journal of dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 2.304
H-Index - 179
eISSN - 1365-2133
pISSN - 0007-0963
DOI - 10.1111/j.1365-2133.1992.tb08052.x
Subject(s) - epidermolysis bullosa acquisita , medicine , dermatology , epidermolysis bullosa , autoimmunity , pathology , autoantibody , immunology , disease , antibody
Summary Epidermolysis bullosa acquisita (EBA) is a rare acquired subepidermal blistering disorder associated with autoimmunity to type VII collagen. Although the full clinical spectrum of EBA is still being defined, it is now known that EBA has greater clinical heterogeneity than previously suggested. We describe a patient with EBA which closely approximated the severity of the recessive form of dystrophic epidermolysis bullosa.