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Panniculitis associated with cutaneous T‐cell lymphoma and cytophagocytic histiocytosis
Author(s) -
ARONSON IRIS K.,
WEST D.P.,
VARIAKOJIS D.,
RONAN S.G.,
IOSSIFIDES I.,
ZEITZ H.J.
Publication year - 1985
Publication title -
british journal of dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 2.304
H-Index - 179
eISSN - 1365-2133
pISSN - 0007-0963
DOI - 10.1111/j.1365-2133.1985.tb02296.x
Subject(s) - medicine , panniculitis , malignant histiocytosis , malignancy , lymphoma , histiocytosis , dermatology , pathology , cutaneous t cell lymphoma , langerhans cell histiocytosis , mycosis fungoides , histiocyte , disease
SUMMARY A 36‐year‐old woman had a 6‐year history of recurrent panniculitis with development of an angiocentric and angiodestructive cutaneous T‐cell lymphoma (CTCL) of the helper cell phenotype. She subsequently developed a rapidly progressive fatal syndrome characterized by cytophagocytic histiocytosis and hyperlipidaemia. Cytophagocytic histiocytosis has previously been reported in association with panniculitis, malignancy and infection, but not with CTCL and the precise relationship between panniculitis, CTCL, cytophagocytic histiocytosis and hyperlipidemia is unclear.