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Familial primary cutaneous amyloidosis
Author(s) -
NEWTON J. A.,
JAGJIVAN A.,
BHOGAL B.,
McKEE P. H.,
McGIBBON D. H.
Publication year - 1985
Publication title -
british journal of dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 2.304
H-Index - 179
eISSN - 1365-2133
pISSN - 0007-0963
DOI - 10.1111/j.1365-2133.1985.tb00084.x
Subject(s) - amyloidosis , medicine , dermatology , amyloid (mycology) , pathology
SUMMARY Primary cutaneous amyloidosis is uncommon in Europeans. A British family is described in which an extremely rare variant was inherited as an autosomal dominant. The subtlety of physical signs in this family contrasted with the severity of the associated pruritus. Transepidermal elimination of amyloid was a characteristic histological feature.