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Juvenile elastoma and osteopoikilosis (the Buschke‐Ollendorff syndrome)
Author(s) -
MORRISON J. G.L.,
JONES E. WILSON,
MACDONALD D. M.
Publication year - 1977
Publication title -
british journal of dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 2.304
H-Index - 179
eISSN - 1365-2133
pISSN - 0007-0963
DOI - 10.1111/j.1365-2133.1977.tb14251.x
Subject(s) - medicine , dermatology , art history , history
SUMMARY Sixteen patients from seven different families with the Buschke‐OUendorff syndrome have been studied. Osteopoikilosis was found in two‐thirds of the patients radiologically examined and all but two had skin involvement. The predominant clinical pattern consisted of grouped skin coloured papules and discs that were distributed asymmetrically and which usually had presented at an early age. The skin lesions showed the characteristic histological changes of juvenile elastoma which, it is suggested, is the specific dermatological abnormality of the Buschke‐Ollendorff syndrome.