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LINEAR MELORHEOSTOTIC SCLERODERMA
Author(s) -
WAGERS LAWRENCE T.,
YOUNG ALEX W.,
RYAN STEPHEN F.
Publication year - 1972
Publication title -
british journal of dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 2.304
H-Index - 179
eISSN - 1365-2133
pISSN - 0007-0963
DOI - 10.1111/j.1365-2133.1972.tb02232.x
Subject(s) - library science , medicine , history , classics , art history , computer science
Summary.— A case of melorheostosis with overlying skin changes is reported This skin lesion is best termed linear melorheostotic scleroderma to differen tiate it from true linear scleroderma. It is characterized by proliferation into the subcutaneous fat of normal‐appearing collagen and elastic tissue in lobes and lobules producing an irregular junction between dermis and subcutaneous fat. The association of linear melorheostatic scleroderma with melorheostosis results in a unique symptom complex which is more disabling than melorheo stosis alone. It is likely that linear melorheostatic scleroderma represents skin involvement by the same proliferation disorder that produces the bony hyperostosis.