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Cardiac arrest under anaesthesia in a child with previously undiagnosed Jervell and Lange‐Nielsen syndrome
Author(s) -
HOLLAND J. J.
Publication year - 1993
Publication title -
anaesthesia
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.839
H-Index - 117
eISSN - 1365-2044
pISSN - 0003-2409
DOI - 10.1111/j.1365-2044.1993.tb06857.x
Subject(s) - medicine , anesthesia , takotsubo syndrome , long qt syndrome , cardiology , cardiomyopathy , heart failure , qt interval
Summary A 7‐year‐old Sikh boy with a history of syncopal attacks and congenital deafness was admitted for elective adenoidectomy and examination of his ears under general anaesthesia. Immediately after induction of anaesthesia an E cg demonstrated T wave inversion in the CM 5 lead. The child subsequently developed multifocal ventricular extrasystoles and later, ventricular fibrillation. Deftbrillation was achieved using two 50 J DC shocks. A 12‐lead ECG performed later demonstrated a prolonged Q‐Tc interval (0.52s). The child was diagnosed as having the Jervell and Lange‐Nielsen syndrome.