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‘Leopard’ syndrome
Author(s) -
RODRIGO M. R. C.,
CHENG C. H.,
TAI Y. T.,
O'DONNELL D.
Publication year - 1990
Publication title -
anaesthesia
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.839
H-Index - 117
eISSN - 1365-2044
pISSN - 0003-2409
DOI - 10.1111/j.1365-2044.1990.tb14499.x
Subject(s) - medicine , abnormality , clinical significance , cardiomyopathy , disease , leopard , pediatrics , cardiology , heart failure , psychiatry , paleontology , biology
Summary ‘Leopard’ syndrome is a rare inherited disorder associated with a high prevalence of cardiac abnormalities. General anaesthesia for dental treatment in a patient who had cardiomyopathy and bizarre electrocardiographs abnormalities associated with this syndrome is described. A thorough cardiac assessment is advised in a patient with multiple lentigines, although no clinical symptoms or signs may be found. Even if no cardiac abnormality is found before it is better to re‐assess the patient, since abnormalities may develop later. The assessment should be repeated if any abnormality was detected before but without clinical significance, since the disease is progressive and may progress more rapidly in some patients than in others.