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Blue Rubber‐Bleb Nevus Syndrome: Report of a Case Associated with Osteoid Osteomas
Author(s) -
Palleschi Giovanni Maria,
Torchia Daniele,
Fabbri Paolo
Publication year - 2005
Publication title -
the journal of dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.9
H-Index - 65
eISSN - 1346-8138
pISSN - 0385-2407
DOI - 10.1111/j.1346-8138.2005.tb00804.x
Subject(s) - osteoid , medicine , dermatology , pathology
Blue rubber‐bleb nevus syndrome (BRBNS), or Bean's syndrome, is a rare angiomatosis characterized by multiple cavernous hemangiomas of the skin, mucosae and frequently of other sites. A 49‐year‐old male patient had been affected since birth by multiple angiomas localized in the skin, lips, oral cavity, cranial theca, and central nervous system; intrauterine rupture of angiomas in the right parietal lobe had caused partial hypotrophic paralysis of the left hemisoma. In addition to BRBNS, the patient was affected by three osteoid osteomas: this never‐described clinical association is here discussed.