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A Case of Generalized Pustular Psoriasis Associated with Turner Syndrome
Author(s) -
Kawakami Yoshio,
Oyama Noritaka,
Kishimoto Kazuhiro,
Yamazaki Keiji,
Nishibu Akiko,
Nakamura Koichiro,
Hoshi Satoshi,
Kaneko Fumio
Publication year - 2004
Publication title -
the journal of dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.9
H-Index - 65
eISSN - 1346-8138
pISSN - 0385-2407
DOI - 10.1111/j.1346-8138.2004.tb00498.x
Subject(s) - generalized pustular psoriasis , psoriasis , medicine , dermatology , pustular psoriasis , erythema , family history , surgery
We report a 27‐year‐old Japanese woman with Turner syndrome who had generalized pustular psoriasis of the von Zumbusch type. She developed a febrile diffuse erythema and pustular eruption without any history of preceding psoriasis vulgaris or drug ingestion. Oral treatment with 3.2 mg/kg cyclosporin per day successfully resulted in rapid improvement, followed by a complete remission. To our knowledge, this is the first report describing the unusual coexistence of these two systemic disorders. We discuss a hormone imbalance that might have contributed to the predisposition to pustular psoriasis and difficulties in the management of the patent's treatment.