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Klippel‐Trenaunay Syndrome with a Life‐Threatening Thromboembolic Event
Author(s) -
Aggarwal Kamal,
Jain Vijay K.,
Gupta Sanjeev,
Aggarwal Hari K.,
Sen Jyotsna,
Goyal Vishal
Publication year - 2003
Publication title -
the journal of dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.9
H-Index - 65
eISSN - 1346-8138
pISSN - 0385-2407
DOI - 10.1111/j.1346-8138.2003.tb00378.x
Subject(s) - klippel trenaunay syndrome , medicine , varicose veins , congenital disorder , pulmonary embolism , venous thrombosis , klippel trenaunay weber syndrome , thrombosis , muscle hypertrophy , surgery , soft tissue , cardiology
Klippel‐Trenaunay syndrome is a congenital disorder characterised by the triad of cutaneous vascular nevi, soft tissue or bony hypertrophy, and varicose veins or venous malformations involving one or more extremities. An incidence of venous thromboembolism of up to 22% has been reported in this disorder. Also reported but rare is the development of trophic changes. Herein, we report the case of a male with Klippel‐Trenaunay syndrome, deep vein thrombosis, venous ulceration, and death due to recurrent pulmonary embolism.