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Spectrum of Reticulate Flexural and Acral Pigmentary Disorders in Northern India
Author(s) -
Dhar Sandipan,
Kanwar Amrinder J.,
Jebraili Roghieh,
Dawn Goutam,
Das Ashim
Publication year - 1994
Publication title -
the journal of dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.9
H-Index - 65
eISSN - 1346-8138
pISSN - 0385-2407
DOI - 10.1111/j.1346-8138.1994.tb01801.x
Subject(s) - reticulate , dermatology , penetrance , medicine , anatomy , biology , genetics , paleontology , phenotype , gene
Reticulate pigmentary disorders are rare in India. Only 15 cases of reticulate acropigmentation of Kitamura (RAPK) and 9 cases of Dowling‐Degos disease (DDD) have been reported previously. To the best of our knowledge, there has been no earlier report of acropigmentation of Dohi. We herein describe 10 patients with various reticulate pigmentary abnormalitis: 6 with RAPK, 2 with DDD, 1 with RAPK‐DDD overlap, and 1 with acropigmentation of Dohi. Palmar pits and/or breaks in epidermal ridge pattern were absent in 2 of 6 patients with RAPK A 23‐year‐old male patient had RAPK‐DDD overlap. Periorbital pigmentation and pigmentation over the mucosal surface of the prepuce and corona of the glans penis were some unique features observed in this patient. His sister and mother had RAPK and DDD, respectively. We concluded that RAPK and DDD are varying manifestations of a single entity. Their presence in other family members probably depends on the degree of penetrance.