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Prominent Telangiectasia Associated with Marked Bleeding in CREST Syndrome
Author(s) -
Ueda Masumi,
Abe Yoshiko,
Fujiwara Hideki,
Fujimoto Wataru,
Arakawa Kenzo,
Arata Jirô,
Yoshioka Toshifumi,
Tomoda Jun,
Katayama Haruko
Publication year - 1993
Publication title -
the journal of dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.9
H-Index - 65
eISSN - 1346-8138
pISSN - 0385-2407
DOI - 10.1111/j.1346-8138.1993.tb03856.x
Subject(s) - telangiectases , telangiectasia , crest syndrome , medicine , sclerodactyly , crest , dermatology , larynx , esophagus , pathology , anatomy , calcinosis , disease , connective tissue disease , autoimmune disease , physics , quantum mechanics , calcification
A 64‐year‐old woman with CREST syndrome developed prominent telangiectases mimicking hereditary hemorrhagic telangiectasia (HHT) of Osler‐Rendu‐Weber. We have been following her since she first came to us with discrete telangiectatic mats and Raynaud's phenomenon 11 years ago. Telangiectatic lesions have been seen on her larynx and esophagus in addition to commonly affected sites. She has experienced spontaneous epistaxis and marked bleeding from the lesions on her lips, oral mucous membrane, and soles. This case illuminates new aspects of telangiectasia in CREST syndrome.