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Liver and lung transplantation in cystic fibrosis: an adult cystic fibrosis centre's experience
Author(s) -
Sivam S.,
AlHindawi Y.,
Di Michiel J.,
Moriarty C.,
Spratt P.,
Jansz P.,
Malouf M.,
Plit M.,
Pleass H.,
Havryk A.,
Bowen D.,
Haber P.,
Glanville A. R.,
Bye P. T. P.
Publication year - 2016
Publication title -
internal medicine journal
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.596
H-Index - 70
eISSN - 1445-5994
pISSN - 1444-0903
DOI - 10.1111/imj.13126
Subject(s) - medicine , cystic fibrosis , liver transplantation , lung , lung transplantation , liver disease , transplantation , lung disease , gastroenterology , surgery
Liver disease develops in one‐third of patients with cystic fibrosis ( CF ). It is rare for liver disease to have its onset after 20 years of age. Lung disease, however, is usually more severe in adulthood. A retrospective analysis was performed on nine patients. Three patients required lung transplantation approximately a decade after liver transplant, and another underwent combined liver and lung transplants. Four additional patients with liver transplants are awaiting assessment for lung transplants. One patient is awaiting combined liver and lung transplants. With increased survival in CF , several patients may require more than single organ transplantation.