Premium
Dermatofibrosarcoma protuberans with fibrosarcomatous transformation: our experience, molecular evaluation of selected cases, and short literature review
Author(s) -
Lopez Liurka V.,
Yatsenko Svetlana A.,
Burgess Melissa,
Schoedel Karen,
Rao Uma N. M.
Publication year - 2019
Publication title -
international journal of dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.677
H-Index - 93
eISSN - 1365-4632
pISSN - 0011-9059
DOI - 10.1111/ijd.14462
Subject(s) - dermatofibrosarcoma protuberans , medicine , dermatofibrosarcoma , dermatology
Abstract Dermatofibrosarcoma protuberans with fibrosarcomatous transformation (DFSP‐FS) is a higher grade tumor arising from dermatofibrosarcoma protuberans (DFSP). Recent literature highlights its impact on recurrence rates, metastatic rates, and survival. In this article, we aim to describe our experience with 13 cases of DFSP‐FS in terms of pathologic findings, molecular alterations, clinical outcomes, management, and also perform a short recent literature review.