Premium
Echocardiographic diagnosis of Shone’s syndrome
Author(s) -
Zhang Xin,
Ma Guiqin,
Zheng Lin,
Zhang Hongju,
Sun Yan,
Li Jingya,
Ma Ning
Publication year - 2020
Publication title -
echocardiography
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.404
H-Index - 62
eISSN - 1540-8175
pISSN - 0742-2822
DOI - 10.1111/echo.14899
Subject(s) - coarctation of the aorta , medicine , cardiology , mitral valve , supravalvular aortic stenosis , stenosis , mitral valve stenosis , heart disease , disease , aorta
Shone’s syndrome is a rare congenital heart disease that includes 4 cardiovascular anomalies: supravalvular mitral ring, parachute mitral valve, subaortic stenosis, and coarctation of the aorta. Early diagnosis and treatment result in better outcomes. Echocardiography plays an important role in the diagnosis and is the optimal examination for detecting this disease. Pressure gradients are often unreliable and inaccurate; thus, careful anatomical observation of the left ventricular inflow and outflow tracts, particularly the mitral valve, is vital for accurate diagnosis and planning appropriate management. Herein, we describe 9 cases of Shone’s syndrome, diagnosed with echocardiography and treated surgically.