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Ostium primum atrial septal defect with persistent left superior vena cava opening into unroofed coronary sinus—A rare entity
Author(s) -
Garg Ashok,
Agrawal Deepak,
Mishra Deepika,
Sharma Gyarsi Lal
Publication year - 2019
Publication title -
echocardiography
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.404
H-Index - 62
eISSN - 1540-8175
pISSN - 0742-2822
DOI - 10.1111/echo.14408
Subject(s) - persistent left superior vena cava , coronary sinus , medicine , cardiology , primary interatrial foramen , atrial septum , ostium , left atrium , foramen secundum , patent foramen ovale , atrial fibrillation , migraine
Raghib syndrome is a rare developmental complex consisting of termination of the left superior vena cava in the left atrium, absence of the coronary sinus, and an atrial septal defect commonly located at the posterior‐inferior angle of the atrial septum. This complex was considered unique to Raghib syndrome; however, cases with a normal atrial septum have been reported where the orifice of the unroofed coronary sinus functions as the inter‐atrial communication. Our patient demonstrated an isolated persistent left superior vena cava draining into the left atrium through unroofed coronary sinus and presence of ostium primum atrial septal defect.