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Cor triatriatum dexter with right ventricular hypoplasia: Role of multimodality imaging in decision making
Author(s) -
Rao Sruti,
Suntharos Patcharapong,
Najm Hani,
Komarlu Rukmini
Publication year - 2018
Publication title -
echocardiography
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.404
H-Index - 62
eISSN - 1540-8175
pISSN - 0742-2822
DOI - 10.1111/echo.14175
Subject(s) - sinus venosus , medicine , septum secundum , cardiology , asymptomatic , tricuspid valve , ventricle , hypoplasia , pulmonic stenosis , cor triatriatum , stenosis , atrial fibrillation , left atrium
Cor Triatriatum Dexter ( CTD ) is a rare congenital anomaly involving the systemic venous valves. Failure of regression of the right‐sided sinus venosus valve leads to abnormal septation of the right atrium and a variety of right atrial and tricuspid valve obstructive lesions. The presentation can be varied ranging from asymptomatic to persistent neonatal cyanosis. We describe a late diagnosis of CTD in a 10‐month‐old male with persistent hypoxia despite balloon valvuloplasty for mild pulmonic valve stenosis with a large secundum atrial septal defect and a mildly hypoplastic right ventricle.