Coronary artery fistula detected with transesophageal echocardiography: An unexpected cause of pulmonary hypertension and chest pain

Coronary artery fistulae are congenital cardiac abnormalities characterized by an abnormal communication between a coronary artery and a cardiac chamber, systemic or pulmonary vessel. Most of the cases are asymptomatic and are discovered incidentally during an angiography. We describe a rare case of a right coronary artery fistula draining to the right atrium, manifesting in chest pain and pulmonary arterial hypertension ( PAH ). The fistula was detected on transesophageal echocardiography during the workup for PAH .