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Multimodality imaging of scimitar syndrome in adults: A report of four cases
Author(s) -
Ngai Calvin,
Freedberg Robin S.,
Latson Larry,
Argilla Michael,
Benenstein Ricardo J.,
Vainrib Alan F.,
Donnino Robert,
Saric Muhamed
Publication year - 2018
Publication title -
echocardiography
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.404
H-Index - 62
eISSN - 1540-8175
pISSN - 0742-2822
DOI - 10.1111/echo.14124
Subject(s) - scimitar syndrome , medicine , asymptomatic , inferior vena cava , cardiology , radiology , lung
Partial anomalous pulmonary venous return (PAPVR) comprises a group of congenital cardiovascular anomalies associated with pulmonary venous flow directly or indirectly into the right atrium. Scimitar syndrome is a variant of PAPVR in which the right lung is drained by right pulmonary veins connected anomalously to the inferior vena cava. Surgery is the definitive treatment for scimitar syndrome. However, it is not always necessary as many patients are asymptomatic, have small left‐to‐right shunts, and enjoy a normal life expectancy without surgery. We report multimodality imaging in four adults with scimitar syndrome and the implications for management of this rare syndrome.