Premium
Shone's syndrome: Insights from three‐dimensional echocardiography
Author(s) -
Vivas Martín F.,
Politi María T.,
Riznyk Laura M.,
Castro María F.,
Avegliano Gustavo,
Ronderos Ricardo
Publication year - 2018
Publication title -
echocardiography
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.404
H-Index - 62
eISSN - 1540-8175
pISSN - 0742-2822
DOI - 10.1111/echo.13787
Subject(s) - mitral valve , cardiology , medicine , stenosis , mitral valve stenosis , mitral valve replacement
Shone's syndrome is a rare congenital anomaly defined as the presence of at least two of the following heart obstructions: a mitral supravalvular ring, a “parachute” mitral valve stenosis, subaortic stenosis, and aortic coarctation. A 58‐year‐old man presented with a mitral ring and a “parachute” mitral valve on two‐dimensional transthoracic echocardiography, raising suspicion of Shone's syndrome. Three‐dimensional transesophageal echocardiography revealed a subannular mitral ring inserted directly on the mitral leaflets, thus acting as a “valvar ring.” This distinction can have therapeutic implications as a “valvar” mitral ring could require valve repair or replacement, instead of simple resection.