Premium
Isolated drainage of right superior vena cava into left atrium: A rare etiology of childhood central cyanosis
Author(s) -
Rakha Shaimaa,
Abuelkheir MohamedMagdy,
Elgamal MohamedAdel F.
Publication year - 2017
Publication title -
echocardiography
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.404
H-Index - 62
eISSN - 1540-8175
pISSN - 0742-2822
DOI - 10.1111/echo.13625
Subject(s) - medicine , intracardiac injection , right atrium , crying , etiology , radiology , persistent left superior vena cava , left atrium , superior vena cava , embolization , surgery , cardiology , coronary sinus , psychiatry , atrial fibrillation
Isolated right superior vena cava drainage into the left atrium ( RSVC ‐ LA ) is an extremely rare anomaly in the absence of other cardiac or extracardiac abnormalities. The clinical and echocardiographic diagnosis is considered challenging. We report a female infant with cyanosis on crying who was diagnosed as isolated RSVC ‐ LA using conventional and contrast echocardiography, but further confirmation was possible via multidetector CT . The surgical correction was performed with smooth postoperative recovery. In conclusion, isolated RSVC ‐ LA must be in the differential diagnosis of cyanosis in the absence of intracardiac anomalies. Surgical correction is necessary management to guard against brain abscesses or paradoxical embolization.