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Siblings with Idiopathic Left Atrial Appendage Ostial Stenosis and Cor Triatriatum
Author(s) -
Okada Seigo,
Ishiguchi Yukiko,
Moritoh Yuji,
Shohi Mayuko,
Nakagawa Naomi,
Okamoto Kengo,
Kamada Masahiro
Publication year - 2016
Publication title -
echocardiography
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.404
H-Index - 62
eISSN - 1540-8175
pISSN - 0742-2822
DOI - 10.1111/echo.13221
Subject(s) - cor triatriatum , medicine , cardiology , stenosis , ostium , atrial fibrillation , left atrium
Isolated left atrial appendage ( LAA ) ostial stenosis is a very rare entity found coincidentally in adults by transesophageal echocardiography. A 3‐month‐old healthy infant was suspected as having cor triatriatum. His brother had a history of surgical treatment of cor triatriatum. A cardiac catheterization revealed a narrowed ostium of the LAA and confirmed the echocardiographic diagnosis of isolated LAA ostial stenosis. This is the first pediatric case of idiopathic LAA ostial stenosis. The siblings called our attention to the differential diagnosis and the etiopathogenesis between LAA ostial stenosis and cor triatriatum.