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Ectopia Cordis with a Double Outlet Right Ventricle, Large Ventricular Septal Defect, Malposed Great Arteries and Left Ventricular Hypoplasia
Author(s) -
Malik Rabiya,
Zilberman Mark V.,
Tang Liwen,
Miller Susan,
Pandian Natesa G.
Publication year - 2015
Publication title -
echocardiography
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.404
H-Index - 62
eISSN - 1540-8175
pISSN - 0742-2822
DOI - 10.1111/echo.12843
Subject(s) - medicine , hypoplasia , ventricle , intracardiac injection , double outlet right ventricle , great arteries , cardiology , anatomy
Ectopia cordis, defined as partial or complete displacement of the heart outside of the thoracic cavity, is a rare congenital malformation. If not surgically corrected during the early years of life, ectopia cordis can prove to be a fatal abnormality. However, due to the presence of multiple intracardiac and extracardiac malformations, a corrective surgery might not always be successful. The pathology of ectopia cordis with a double outlet right ventricle, large ventricular septal defect, malposed great arteries and left ventricular hypoplasia is discussed, highlighting the complexities involved in such a rare disorder.