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Isolated Supravalvular Pulmonary Stenosis: A Rare Echocardiographic Finding
Author(s) -
Maffè Stefano,
Dellavesa Pierfranco,
Paffoni Paola,
Ze Franco,
Cucchi Lorenzo,
Paino Anna Maria,
Bergamasco Luca,
Baduena Lara,
Franchetti Pardo Nicolò,
Zanetta Marco,
Parravicini Umberto
Publication year - 2014
Publication title -
echocardiography
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.404
H-Index - 62
eISSN - 1540-8175
pISSN - 0742-2822
DOI - 10.1111/echo.12612
Subject(s) - supravalvular aortic stenosis , medicine , cardiology , stenosis , radiology
Isolated supravalvular pulmonary stenosis is a rare finding, usually evidenced in the pediatric age. Here, we report a case of a 76‐year‐old patient with isolated, severely obstructive, pulmonary supravalvular stenosis. The peculiarity of the present case is the paucity of symptoms and lack of changes in right heart sections, despite of the importance of stenosis. The report confirms the utility of transthoracic two‐ and three‐dimensional echocardiography and transesophageal echocardiography in the detection and quantification of this rare anomaly.