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A Coronary–Pulmonary Artery Fistula with Giant Aneurysm in a Child with Ventricular Septal Defect with Pulmonary Atresia
Author(s) -
Mahimaiha Jayaranganath,
Patra Soumya,
Mandikal Kodanda Rama Sastry Usha,
Subramaniam Anand,
Agrawal Navin,
Nanjappa Manjunath Cholenahally
Publication year - 2014
Publication title -
echocardiography
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.404
H-Index - 62
eISSN - 1540-8175
pISSN - 0742-2822
DOI - 10.1111/echo.12496
Subject(s) - medicine , pulmonary atresia , cardiology , pulmonary artery , fistula , atresia , aneurysm , radiology
Mini‐Abstract Pulmonary atresia with ventricular septal defect accounts for about 2% of all congenital heart diseases. Aortopulmonary collaterals are the usual source of pulmonary blood flow. Coronary–pulmonary artery fistula is a rare and sole source of pulmonary blood flow. We are reporting a case of a 6‐year‐old girl who presented with severe cyanosis, clubbing, and effort intolerance. Echocardiography demonstrated a large subaortic ventricular septal defect and pulmonary atresia with confluent pulmonary arteries. It also revealed the presence of a coronary–pulmonary artery fistula along with a giant coronary artery aneurysm. These findings were confirmed by an aortic root angiogram. She was referred for intra‐ cardiac repair.