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Spiral Hypertrophic Cardiomyopathy as Detected by Cardiac Magnetic Resonance
Author(s) -
Amin Nessim,
Williams Ronald B.,
Yarmozik June A.,
Biederman Robert W.W.
Publication year - 2014
Publication title -
echocardiography
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.404
H-Index - 62
eISSN - 1540-8175
pISSN - 0742-2822
DOI - 10.1111/echo.12443
Subject(s) - hypertrophic cardiomyopathy , muscle hypertrophy , cardiology , concentric hypertrophy , medicine , magnetic resonance imaging , contractility , cardiomyopathy , spiral (railway) , left ventricular hypertrophy , heart failure , radiology , blood pressure , mathematical analysis , mathematics
Hypertrophic cardiomyopathy (HCM) is a genetically determined heart muscle disease; characterized by left ventricular hypertrophy. Spiral HCM is described as having a counterclockwise rotation pattern of hypertrophy along with variable degrees of fibrosis. A 34‐year‐old female presented with symptoms suggestive of heart failure. Echocardiography showed concentric left ventricular hypertrophy with normal contractility. Cardiac MRI showed asymmetric septal hypertrophy with mid‐cavity obliteration and a spiral pattern of variably increasing wall thickness. Late gadolinium enhancement demonstrated several areas of abnormal post‐gadolinium uptake. We report a case of spiral HCM. We should consider cardiovascular magnetic resonance as the reference standard for diagnosing HCM.