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Ebstein's Anomaly with Subpulmonary Obstruction– A Rare Association
Author(s) -
Singh Bhupinder,
Subramanyan Anand,
Jayaranganath M.,
Manjunath C. N.
Publication year - 2013
Publication title -
echocardiography
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.404
H-Index - 62
eISSN - 1540-8175
pISSN - 0742-2822
DOI - 10.1111/echo.12205
Subject(s) - tricuspid valve , medicine , ebstein anomaly , ventricle , cardiology , shunt (medical)
Ebstein's anomaly comprises a wide spectrum of congenital cardiac abnormalities involving the tricuspid valve (TV) apparatus and the architecture of the morphological right ventricle (RV). We report a case of Ebstein's anomaly in a 3‐year‐old boy having a unique association with severe subpulmonic obstruction caused by tethered and dysplastic anterior tricuspid leaflet (ATL), and a large ventricular septal defect. In view of poorly functioning RV, the baby was planned for a bidirectional Glenn shunt with subsequent Fontan completion.