Premium
Coccygeal polypoid eccrine nevus associated with imperforate anus and unilateral multicystic kidney dysplasia
Author(s) -
Frouin Eric,
Riviere Benjamin,
Maillet Olivier,
Willems Marjolaine,
Kalfa Nicolas,
Costes Valerie,
Bessis Didier
Publication year - 2016
Publication title -
journal of cutaneous pathology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.597
H-Index - 75
eISSN - 1600-0560
pISSN - 0303-6987
DOI - 10.1111/cup.12718
Subject(s) - imperforate anus , medicine , multicystic dysplastic kidney , dysplasia , pathology , differential diagnosis , anus , pathological , hamartoma , nevus , anatomy , dermatology , urinary system , melanoma , cancer research
Eccrine nevi are rare hamartomas characterized by an increase in the number or size of eccrine glands. A polypoid form located in the coccygeal area has been described in a few cases and termed coccygeal polypoid eccrine nevus ( CPEN ). No association with internal malformations was reported in any of these cases. We describe herein a case of CPEN associated with imperforate anus and unilateral multicystic kidney dysplasia. We review the clinical and pathological characteristics of CPENs and discuss the differential diagnoses.