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Maffucci syndrome with the spindle cell hemangiomas in the mucosa of the lower lip: a rare case report and literature review
Author(s) -
Cai Yu,
Wang Rong,
Chen XinMing,
Zhao YiFang,
Sun ZhiJun,
Zhao JiHong
Publication year - 2013
Publication title -
journal of cutaneous pathology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.597
H-Index - 75
eISSN - 1600-0560
pISSN - 0303-6987
DOI - 10.1111/cup.12131
Subject(s) - medicine , hemangioma , tongue , pathology , oral mucosa , lower lip , oral cavity , dermatology , surgery , dentistry
The presence of non‐cutaneous vascular lesions in the syndrome of multiple enchondromas and subcutaneous hemangiomas, also named Maffucci syndrome, is exceedingly rare. Until now, non‐cutaneous vascular lesions have been described in nine patients, while only three cases were present in the oral cavity; they were found in the tongue in two patients and in the lower lip in one patient. Herein, we report the second case of vascular lesions localized in the mucosa of lower lip in a patient with Maffucci syndrome. Histopathologic examination showed spindle cell hemangioma.