Open AccessPresacral and intrathoracic extramedullary hematopoiesis in a patient with β thalassemia minor
Author(s) -
Lalueza Antonio,
Silva Carlos Patricio,
AlcaláGaliano Andrea,
Arrieta Estibaliz,
Cánovas José Miguel,
Calero Maria Rosa,
Álvarez Carlos
Publication year - 2018
Publication title -
the clinical respiratory journal
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.789
H-Index - 33
eISSN - 1752-699X
pISSN - 1752-6981
DOI - 10.1111/crj.12490
Subject(s) - extramedullary hematopoiesis , medicine , thalassemia , bone marrow , haematopoiesis , hematologic disease , cytology , epigastric pain , radiology , pathology , disease , surgery , genetics , stem cell , biology , vomiting
Extramedullary hematopoiesis (EMH) is a rare disease characterized by the presence of hematopoietic elements outside the bone marrow as a compensatory phenomenon in several hematological diseases, including thalassemia. We report a 64‐year‐old man with epigastric pain of 3‐months' duration radiated to the back. Imaging workup showed multiple paravertebral, retrosternal and presacral masses. Cytology findings obtained by CT‐guided FNAC were compatible with the diagnosis of EMH. Peripheral blood smear confirmed the presence of β‐thalassemia.