Open AccessSpontaneous bilateral haemothorax as presentation of primary pleural epithelioid haemangioendothelioma
Author(s) -
Ferreiro Lucía,
SanJosé Esther,
SuárezAntelo Juan,
Abdulkader Ihab,
MartínezdeAlegría Anxo,
GonzálezBarcala FranciscoJavier,
Valdés Luis
Publication year - 2017
Publication title -
the clinical respiratory journal
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.789
H-Index - 33
eISSN - 1752-699X
pISSN - 1752-6981
DOI - 10.1111/crj.12421
Subject(s) - medicine , epithelioid hemangioendothelioma , thoracoscopy , malignancy , presentation (obstetrics) , radiology , angiosarcoma , surgery , pathology , immunohistochemistry
Abstract Pleural epithelioid haemangioendothelioma (EHE) is a rare tumour that originates in the vascular endothelium with an intermediate degree of malignancy between haemangioma and angiosarcoma. Smoking and asbestos exposure are unproven risk factors and diagnosis is usually confirmed by thoracoscopy, since pleural fluid (PF) cytology is often not conclusive. Immunohistochemistry can also help to confirm the diagnosis. We report an 85‐year‐old patient with bilateral pleural EHE diagnosed by thoracoscopy, who debuted with a spontaneous bilateral haemothorax, the second described so far, and we conducted a thorough review of the literature to describe the clinical, radiological and prognostic features, as well as the PF, of this rare tumour.