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High Le Fort I osteotomy for correction of mid‐face deformity in Crouzon syndrome
Author(s) -
Nakajima Yasumichi,
Nakano Hiroyuki,
Sumida Tomoki,
Yamada Tomohiro,
Inoue Kazuya,
Sugiyama Goro,
Mishima Katsuaki,
Mori Yoshihide
Publication year - 2016
Publication title -
congenital anomalies
Language(s) - English
Resource type - Journals
eISSN - 1741-4520
pISSN - 0914-3505
DOI - 10.1111/cga.12168
Subject(s) - crouzon syndrome , medicine , nasion , osteotomy , deformity , orthodontics , overjet , maxillary hypoplasia , maxilla , malocclusion , orthognathic surgery , dentistry , craniofacial , surgery , distraction osteogenesis , distraction , neuroscience , psychiatry , biology
An 18‐year‐old woman with mild Crouzon syndrome was referred with malocclusion and mandibular protrusion. Examination revealed Class III canine and molar relationships, hypoplastic maxilla, 1‐mm overbite, and −2‐mm overjet. Analysis showed 69° sella‐nasion‐A, 73.6° sella‐nasion‐B, and −4.6° A point‐nasion‐B point angles. Polysomnography revealed respiratory disturbance and 6.3% oxygen desaturation indices of 5.4/h and 9.0/h. We performed double‐jaw surgery using high Le Fort I osteotomy and bilateral sagittal split ramus osteotomy for midfacial deformity correction. Twelve months post‐surgery, her measures were 70.8°, 72°, −1.2°, 3.0/h, and 6.1/h, respectively. Esthetics were satisfactory. High Le Fort I osteotomy is effective for midfacial deformity correction in patients with Crouzon syndrome.