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Review shows that implementing a nationwide protocol for congenital diaphragmatic hernia was a key factor in reducing mortality and morbidity
Author(s) -
Storme L,
Boubnova J,
Mur S,
Pog L,
Sharma D,
Aubry E,
Sfeir R,
Vaast P,
Rakza T,
Benachi A
Publication year - 2018
Publication title -
acta paediatrica
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.772
H-Index - 115
eISSN - 1651-2227
pISSN - 0803-5253
DOI - 10.1111/apa.14169
Subject(s) - medicine , congenital diaphragmatic hernia , pulmonary hypoplasia , pediatrics , intensive care medicine , hypoplasia , multidisciplinary team , multidisciplinary approach , protocol (science) , diaphragmatic hernia , hernia , surgery , pathology , gestation , pregnancy , fetus , genetics , nursing , alternative medicine , biology , social science , sociology
Abstract The French Rare Disease Reference Center for congenital diaphragmatic hernia ( CDH ) was created in 2008, to implement a national protocol for foetuses and children with this serious condition. Neonatal mortality from CDH is 30‐40%, mainly due to pulmonary hypoplasia and persistent pulmonary hypertension, and half of those who live have high respiratory, nutritional and digestive morbidity. CDH management requires long‐term and specialised multidisciplinary care. It has been well established that a standardised management protocol improves the prognosis of children with CDH . Conclusion Organising health care and implementing a nationwide French protocol were key factors for reducing mortality and morbidity from CDH .