Open AccessLate‐onset severe long QT syndrome
Author(s) -
Asatryan Babken,
Schaller André,
Bartholdi Deborah,
MedeirosDomingo Argelia
Publication year - 2018
Publication title -
annals of noninvasive electrocardiology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.494
H-Index - 48
eISSN - 1542-474X
pISSN - 1082-720X
DOI - 10.1111/anec.12517
Subject(s) - medicine , asymptomatic , long qt syndrome , torsades de pointes , sudden death , sudden cardiac death , qt interval , short qt syndrome , pediatrics , family history , cardiology
We report a case of torsades de pointes arrhythmia as the first manifestation of congenital Long QT syndrome in a 77‐year‐old man with family history of sudden unexplained death. This case illustrates the importance of vigilant clinical assessment and genetic counseling in families with sudden death in order to identify properly asymptomatic relatives at risk for cardiac events. It also demonstrates that Long QT syndrome can still manifest with potentially fatal arrhythmias late in life in previously asymptomatic elderly patients.