Open AccessEKG Pattern of Brugada Syndrome and Sudden Infant Death Syndrome—Is It Time to Review the Diagnostic Criteria? Case Report and Review of Literature
Author(s) -
Franco Emiliana,
Dias Andre,
Teresa Daniele,
Hebert Kathy
Publication year - 2014
Publication title -
annals of noninvasive electrocardiology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.494
H-Index - 48
eISSN - 1542-474X
pISSN - 1082-720X
DOI - 10.1111/anec.12086
Subject(s) - medicine , brugada syndrome , sudden infant death syndrome , sudden cardiac death , hyperkalemia , cardiology , pediatrics , sudden death , right bundle branch block , electrocardiography
Brugada Syndrome (BrS) is a cardiac disorder characterized by incomplete right bundle‐branch block and ST elevations in the anterior precordial leads especially V 1 –V 3 , associated with an increased risk for sudden cardiac death (SCD) in young adults. Our case describes a patient with family history of sudden infant death syndrome (SIDS) who presented with a Brugada pattern unmasked by severe hyperkalemia and diabetic ketoacidosis. Several studies have concluded there may be a genetic link among SIDS, SDC, and BrS resulting from mutations in cardiac ion channel‐related genes. Recognizing SIDS as part of the diagnostic criteria for BrS would help us identifying a significant number of families susceptible to develop SCD (as well as SIDS).