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Successful treatment with intravenous high‐dose immunoglobulin for cardiomyopathy in dermatomyositis complicated with rapid progressive interstitial pneumonia
Author(s) -
Yoshimatsu Yuki,
Kotani Takuya,
Fujiki Youhei,
Oda Katsuhiro,
Kataoka Toshiya,
Yamairi Kazushi,
Hata Kenichiro,
Otani Kenichiro,
Kamimori Takao,
Fujiwara Hiroshi
Publication year - 2019
Publication title -
international journal of rheumatic diseases
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.795
H-Index - 41
eISSN - 1756-185X
pISSN - 1756-1841
DOI - 10.1111/1756-185x.12746
Subject(s) - medicine , dermatomyositis , cardiomyopathy , polymyositis , myocarditis , adverse effect , cardiology , heart failure
Cardiomyopathy and rapid progressive interstitial pneumonia ( IP ) are potentially fatal complications in polymyositis/dermatomyositis. We experienced a dermatomyositis patient with multiple adverse prognostic factors, complicating rapid progressive IP , macrophage activation syndrome ( MAS ), and cardiomyopathy. IP and MAS improved with strong immunosuppressive therapy, despite which cardiomyopathy developed. Therefore, we applied intravenous high‐dose immunoglobulin therapy ( IVI g), and cardiac function improved dramatically. This is the first report to present the effectiveness of IVI g for cardiomyopathy in dermatomyositis.