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Hairy cell leukemia presenting initially with symptoms of B ehçet's disease
Author(s) -
Oksuz Mustafa Ferhat,
Coskun Belkis Nihan,
Tufan Ayse Nur,
Orucoglu Nurdan,
Dalkilic Ediz,
Öztürk Nazlıoğlu Hülya,
Pehlivan Yavuz
Publication year - 2014
Publication title -
international journal of rheumatic diseases
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.795
H-Index - 41
eISSN - 1756-185X
pISSN - 1756-1841
DOI - 10.1111/1756-185x.12370
Subject(s) - medicine , pancytopenia , hairy cell leukemia , vasculitis , lymphoproliferative disease , dermatology , polyarteritis nodosa , behcet's disease , arthritis , pathology , immunology , leukemia , disease , bone marrow
Vasculitis is relatively uncommon in lymphoproliferative disease and may predate the diagnosis of lymphoproliferative disease. Many vasculitides have been associated with hairy cell leukemia ( HCL ), including polyarteritis nodosa ( PAN ) and leukocytoclastic vasculitis. We herein report a case whose initial presentation was like Behçet's disease ( BD ) (arthritis, oral and genital ulcerations, papulopustular skin lesions) in addition to pancytopenia, but turned out to have HCL . Because of the overlap between their symptoms, like oral ulcerations, skin lesions, arthritis and constitutional findings, HCL and BD may mimic each other. We should keep in mind other reasons for vasculitis such as lymphoproliferative disease, especially whose who have hematological abnormalities such as pancytopenia.