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Radiological findings of perivascular epithelioid cell tumour ( PEC oma) of the falciform ligament
Author(s) -
Handa Atsuhiko,
Fujita Kazutoshi,
Kono Tatsuo,
Komori Koji,
Hirobe Seiichi,
Fukuzawa Ryuji
Publication year - 2016
Publication title -
journal of medical imaging and radiation oncology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.31
H-Index - 43
eISSN - 1754-9485
pISSN - 1754-9477
DOI - 10.1111/1754-9485.12460
Subject(s) - falciform ligament , medicine , perivascular epithelioid cell , umbilicus (mollusc) , pathology , anatomy , abdomen , radiology , immunohistochemistry , epithelioid cell
Summary Perivascular epithelioid cell tumour ( PEC oma) encompasses a group of mesenchymal tumours composed of histologically and immunohistochemically distinctive perivascular epithelioid cells. A subset of PEC oma that typically arises from the falciform ligament and/or ligamentum teres is termed clear cell myomelanocytic tumour of the falciform ligament/ligamentum teres. To date, its imaging findings have not been described. Here, we report the first radiological description of a pathologically confirmed tumour. The patient was a 5‐year‐old girl with a palpable abdominal mass. US , CT , MR and FDG ‐ PET revealed a midline, well‐defined, solid anterior abdominal wall tumour below the rectus abdominis and contiguous with the umbilicus that was hypervascular and FDG avid. Awareness of these imaging findings facilitates the diagnosis of this distinctive tumour.