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A case of pneumatosis cystoides intestinalis in connective tissue disease
Author(s) -
Fung Arthur MY,
Ng KaChun,
Tsui Wilson MS,
Wong KwokWa
Publication year - 2016
Publication title -
surgical practice
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.109
H-Index - 10
eISSN - 1744-1633
pISSN - 1744-1625
DOI - 10.1111/1744-1633.12211
Subject(s) - pneumatosis cystoides intestinalis , medicine , pneumoperitoneum , connective tissue , conventional pci , peritonitis , connective tissue disease , rare disease , surgery , disease , pathology , laparoscopy , autoimmune disease , myocardial infarction
Pneumatosis cystoides intestinalis ( PCI ) with spontaneous pneumoperitoneum is a rare but important condition in patients with connective tissue disease. In the present study, we report on a woman with mixed connective tissue disease who presented with PCI , and subsequently symptoms, of chronic intestinal pseudo‐obstruction. Prompt surgical resection of the bowel segment with pneumatosis should be considered to prevent a condition of gas leakage from turning into full‐blown chemical peritonitis.
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