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Japanese guidelines for the management and treatment of generalized pustular psoriasis: The new pathogenesis and treatment of GPP
Author(s) -
Fujita Hideki,
Terui Tadashi,
Hayama Koremasa,
Akiyama Masashi,
Ikeda Shigaku,
Mabuchi Tomotaka,
Ozawa Akira,
Kanekura Takuro,
Kurosawa Michiko,
Komine Mayumi,
Nakajima Kimiko,
Sano Shigetoshi,
Nemoto Osamu,
Muto Masahiko,
Imai Yasutomo,
Yamanishi Kiyofumi,
Aoyama Yumi,
Iwatsuki Keiji
Publication year - 2018
Publication title -
the journal of dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.9
H-Index - 65
eISSN - 1346-8138
pISSN - 0385-2407
DOI - 10.1111/1346-8138.14523
Subject(s) - generalized pustular psoriasis , christian ministry , medicine , psoriasis , pathogenesis , disease , clinical trial , intensive care medicine , dermatology , political science , law
Generalized pustular psoriasis ( GPP ) is a rare disease characterized by recurrent fever and systemic flushing accompanied by extensive sterile pustules. The committee of the guidelines was founded as a collaborative project between the Japanese Dermatological Association and the Study Group for Rare Intractable Skin Diseases under the Ministry of Health, Labour, and Welfare Research Project on Overcoming Intractable Diseases. The aim of the guidelines was to provide current information to aid in the treatment of patients with GPP in Japan. Its contents include the diagnostic and severity classification criteria for GPP , its pathogenesis, and recommendations for the treatment of GPP . Since there are few clinical trial data with high levels of evidence for this rare disease, recommendations by the committee are described in the present guidelines.