Open AccessPredictors of Long-term Outcomes in Patients With Connective Tissue Disease Associated With Pulmonary Arterial Hypertension
Author(s) -
Keiichi I. Nakayama,
Yasuo Nakajima,
Rika Tanaka,
Kenichi Hirata,
Noriaki Emoto
Publication year - 2020
Publication title -
journal of clinical rheumatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.615
H-Index - 50
eISSN - 1536-7355
pISSN - 1076-1608
DOI - 10.1097/rhu.0000000000001447
Subject(s) - medicine , cardiology , proportional hazards model , connective tissue disease , pulmonary hypertension , blood pressure , ctd , stepwise regression , disease , autoimmune disease , oceanography , geology
Pulmonary arterial hypertension (PAH) is a progressive disease characterized by increased pulmonary arterial pressure and pulmonary vascular resistance that can lead to right-sided heart failure. Connective tissue disease-associated PAH (CTD-PAH) often has poorer outcomes than idiopathic or hereditary PAH, suggesting the presence of non-PAH factors that could affect the prognoses. This cohort study aimed to identify prognostic factors for CTD-PAH management.