Open AccessRapunzel Syndrome Complicated by Escherichia coli Sepsis, Bowel Perforation, and Pancreatitis in an 11‐year‐old Malnourished Female
Author(s) -
Daniel Rhea,
Arbuthnot Mary,
Ramireddy Srinivas,
Nair Supriya
Publication year - 2022
Publication title -
jpgn reports
Language(s) - English
Resource type - Journals
ISSN - 2691-171X
DOI - 10.1097/pg9.0000000000000171
Subject(s) - medicine , vomiting , abdominal pain , intussusception (medical disorder) , perforation , sepsis , nausea , pancreatitis , complication , acute pancreatitis , gastroenterology , surgery , weight loss , obesity , materials science , punching , metallurgy
The most common presenting symptoms of Rapunzel syndrome include abdominal pain (37%), nausea and vomiting (33.3%), obstruction (25.9%), and peritonitis (18.3%). Less commonly, patients may present with weight loss (7.4%) or intussusception (7.4%). Exceedingly rare complications of Rapunzel syndrome include gastric ulceration, obstructive jaundice, and acute pancreatitis as well as other malabsorptive‐related complications including protein‐losing enteropathy, iron deficiency, and megaloblastic anemia. This report details the case of an 11‐year‐old female with Rapunzel syndrome complicated by sepsis, a rare complication reported in only 2% of patients.