Open AccessCongenital Chylous Ascites
Author(s) -
Rashid Rafia,
Shafi Ahmed Syed,
Mahmud Salahuddin
Publication year - 2022
Publication title -
jpgn reports
Language(s) - English
Resource type - Journals
ISSN - 2691-171X
DOI - 10.1097/pg9.0000000000000149
Subject(s) - medicine , chylous ascites , octreotide , maldevelopment , lymphatic system , chylomicron , ascites , chyle , parenteral nutrition , rare disease , paracentesis , abdominal cavity , peritoneal cavity , surgery , gastroenterology , somatostatin , disease , pathology , complication , lipoprotein , very low density lipoprotein , cholesterol , anatomy
Congenital chylous ascites (CCAs) are a rare disease that results from the accumulation of chylomicron‐rich lymphatic fluid within the peritoneal cavity due to maldevelopment of the intra‐abdominal lymphatic system. Medium‐chain triglyceride (MCT)‐based diet, total parenteral nutrition (TPN), and repeated paracentesis are considered supportive management for CCA. Cases unresponsive to conservative treatment usually require surgical intervention. We report a case of CCA in a premature neonate treated successfully with intravenous infusion of octreotide (synthetic somatostatin analog), after failing to respond to supportive therapies. Due to the lack of standards in diagnosis and treatment, this disease constitutes a medical challenge, and individual therapy seems to be noteworthy.