Open AccessInflammatory Bowel Disease Manifesting After Surgical Treatment for Hirschsprung Disease
Author(s) -
Levin David N.,
Marcon Margaret A.,
Rintala Risto J.,
Jacobson Dustin,
Langer Jacob C.
Publication year - 2012
Publication title -
journal of pediatric gastroenterology and nutrition
Language(s) - Uncategorized
Resource type - Journals
eISSN - 1536-4801
pISSN - 0277-2116
DOI - 10.1097/mpg.0b013e31824f617a
Subject(s) - medicine , hematochezia , enterocolitis , hirschsprung's disease , fistula , inflammatory bowel disease , disease , surgery , necrotizing enterocolitis , megacolon , gastroenterology , colonoscopy , colorectal cancer , cancer
ABSTRACT Eight children developed chronic inflammatory bowel disease (IBD) 4 to 21 years after surgery for Hirschsprung disease. Three had trisomy 21 and 6 experienced chronic or recurrent enterocolitis. Four had a family history of IBD. Clinical presentation included chronic diarrhea, hematochezia, abscess, and fistula formation. Three required surgery for fistula, stricture, and small bowel obstruction and the other 5 were managed medically. Recognition of this condition may be important in the long‐term follow‐up of children with Hirschsprung disease, and patients who have carried a diagnosis of chronic enterocolitis may warrant further investigation looking for evidence of IBD.