
Acute Recurrent and Chronic Pancreatitis as Initial Manifestations of Cystic Fibrosis and Cystic Fibrosis Transmembrane Conductance Regulator–Related Disorders
Author(s) -
Christina Baldwin,
Melissa Zerofsky,
Meghana Sathe,
David M. Troendle,
Emily R. Perito
Publication year - 2019
Publication title -
pancreas
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.061
H-Index - 104
eISSN - 1536-4828
pISSN - 0885-3177
DOI - 10.1097/mpa.0000000000001350
Subject(s) - cystic fibrosis transmembrane conductance regulator , cystic fibrosis , medicine , pancreatitis , gastroenterology , pancreatic disease , sweat test , potentiator , exocrine pancreatic insufficiency , immunology , pancreas
Recurrent pancreatitis is considered a rare manifestation of cystic fibrosis transmembrane conductance regulator (CFTR) dysfunction; this case series highlights that pancreatitis can be a presenting symptoms of cystic fibrosis (CF) or a CFTR-related disorder (CFTR-RD).