Open AccessCongenital afibrinogenemia
Author(s) -
Stéphanie Malaquin,
Lionel Rebibo,
Cyril Chivot,
Louise Badoux,
Yazine Mahjoub,
Hervé Dupont
Publication year - 2016
Publication title -
medicine
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.59
H-Index - 148
eISSN - 1536-5964
pISSN - 0025-7974
DOI - 10.1097/md.0000000000004150
Subject(s) - medicine , afibrinogenemia , fibrinogen , coagulation disorder , surgery , hematoma , coagulation
Afibrinogenemia is a rare coagulation disorder. Clinical features of spontaneous bleeding, bleeding after minor trauma, or after surgery have been described as well as thrombo-embolic complications. In this article, we presented the case of a 19-year old female with congenital afibrinogenemia who was admitted with a spontaneous intrahepatic hematoma. Conclusions: Supportive treatment including transfusion and fibrinogen administration, associated with repeated packing surgeries and selective embolization, were successfully performed.