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ALCAPA in an Adult with Preserved Left Ventricular Function
Author(s) -
Selzman Craig H.,
Zimmerman Michael A.,
Campbell David N.
Publication year - 2003
Publication title -
journal of cardiac surgery
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.428
H-Index - 58
eISSN - 1540-8191
pISSN - 0886-0440
DOI - 10.1046/j.1540-8191.2003.01908.x
Subject(s) - medicine , left coronary artery , cardiology , pulmonary artery , ventricular function , mitral regurgitation , cardiomyopathy , artery , heart failure
Anomalous origin of the left coronary artery from the pulmonary artery (ALCAPA) is the most common congenital coronary artery defect. Left uncorrected, nearly 90% of patients will die within one year. Without surgical repair, surviving patients are subjected to risks of myocardial ischemia with global cardiomyopathy, chronic mitral regurgitation, and sudden death. We report a case of ALCAPA in a 23‐year‐old female with completely preserved left ventricular function. This article reviews the mechanism of this unusual presentation as well as the therapeutic options for adults presenting with ALCAPA. (J Card Surg 2003; 18:25‐28)