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Infrapatellar Hypertrichosis: An Unusual Cutaneous Manifestation of Juvenile Dermatomyositis
Author(s) -
Piantanida Nicholas A.,
Person Donald A.,
Piantanida Elizabeth W.
Publication year - 2002
Publication title -
pediatric dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.542
H-Index - 73
eISSN - 1525-1470
pISSN - 0736-8046
DOI - 10.1046/j.1525-1470.2002.00050.x
Subject(s) - medicine , juvenile dermatomyositis , hypertrichosis , proximal muscle weakness , dermatology , dermatomyositis , ptosis , inflammatory myopathy , dystrophic calcification , myopathy , calcification , pathology , surgery , biopsy , muscle biopsy
Juvenile dermatomyositis (JDM) is an uncommon inflammatory myopathy with characteristic cutaneous manifestations. Certain clinical features such as cutaneous calcification, lipoatrophy, and generalized hypertrichosis can occur in JDM but are uncommon in the adult form of the disease. We report a young girl who presented with dramatic infrapatellar hypertrichosis along with more classic clinical signs of JDM, including heliotrope periorbital eruption, photosensitivity, and profound proximal muscle weakness. The clinical course was favorable, with improvement of cutaneous and muscular abnormalities after corticosteroid treatment.