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Cutis Marmorata Telangiectatica Congenita: Laser Doppler Fluxmetry Evidence for a Functional Nervous Defect
Author(s) -
Bormann Gisela,
Wohlrab Johannes,
Fischer Matthias,
Marsch Wolfgang Christian
Publication year - 2001
Publication title -
pediatric dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.542
H-Index - 73
eISSN - 1525-1470
pISSN - 0736-8046
DOI - 10.1046/j.1525-1470.2001.018002110.x
Subject(s) - medicine , laser doppler velocimetry , hemodynamics , cardiology , blood flow
We report a 5‐month‐old infant with cutis marmorata telangiectatica congenita (CMTC) without associated abnormalities and unusual hemicorporal vascular markings. Laser Doppler fluxmetry of the involved skin, carried out for the first time, and the measurement of the transcutaneous partial pressure of oxygen indicate a functional disturbance, which may be the expression of an α‐adrenergic innervation deficit of the cutaneous terminal blood vessels.