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Pain Management of Junctional Epidermolysis Bullosa in an 11‐Year‐Old Boy
Author(s) -
Chiu YaoKun,
Prendiville Julie S.,
Bennett Susan M.,
Montgomery Carolyne J.,
Oberlander Tim F.
Publication year - 1999
Publication title -
pediatric dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.542
H-Index - 73
eISSN - 1525-1470
pISSN - 0736-8046
DOI - 10.1046/j.1525-1470.1999.00120.x
Subject(s) - medicine , junctional epidermolysis bullosa (veterinary medicine) , epidermolysis bullosa , dermatology , surgery , pain management , anesthesia , biochemistry , chemistry , mutation , gene
Epidermolysis bullosa is a group of hereditary blistering disorders for which there is no definitive therapy. Wound care is an important component of management. Regular dressing changes are required to protect blistered and eroded skin, and to prevent secondary infection and sepsis. These dressing changes can be very painful for patients with extensive erosions. We report our experience of pain management in an 11‐year‐old boy with severe junctional epidermolysis bullosa. Amitryptiline and cognitive behavioral techniques were effective in relieving chronic pain and discomfort. Oral midazolam 0.33 mg/kg administered 20 minutes prior to baths and dressing changes substantially improved his tolerance of wound care.